Case Report


Pleomorphic adenoma of orbital ectopic lacrimal gland associated with swollen optic disc

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1 Consultant Ophthalmologist, Department of Ophthalmology, North Okkalapa General and Teaching Hospital, Yangon, Myanmar

2 Consultant Pathologist, Department of Pathology, Yangon General Hospital, Yangon, Myanmar

3 Resident Physician, Department of Ophthalmology, National University Hospital, Singapore

Address correspondence to:

Zin May Htoon

Department of Ophthalmology, North Okkalapa General and Teaching Hospital, North Okkalapa Township, Yangon,

Myanmar

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Article ID: 100011Z17ZH2019

doi: 10.5348/100011Z17ZH2019CR

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How to cite this article

Htoon ZM, Thant KK, Zin LS, Naing T. Pleomorphic adenoma of orbital ectopic lacrimal gland associated with swollen optic disc. J Case Rep Images Opthalmol 2019;2:100011Z17ZH2019.

ABSTRACT


Introduction: Pleomorphic adenoma is the most common benign epithelial neoplasm of the lacrimal gland. This is the case report of a 63-year-old lady with pleomorphic adenoma of ectopic lacrimal gland in the superomedial part of orbit.

Case Report: A 63-year-old lady presented with gradually increasing non-axial proptosis of left eye for two years duration. There was downwards and outwards displacement of left eye ball by a hard, palpable mass in the superomedial part of left orbit. The left eye showed relative afferent pupillary defect and swollen optic disc. Computerized tomography demonstrated an extraconal, well-circumscribed mass lesion occupying superomedial part of the left orbit. Complete surgical excision of tumor was performed through anterior orbitotomy. The histopathology showed an encapsulated tumor composed of nests and strands of cuboidal-shaped epithelial cells and myoepithelial cells supported by loose myxoid and hyalinized calcified stroma. The mass was diagnosed “a pleomorphic adenoma arising from ectopic lacrimal gland.”

Conclusion: To our knowledge, this is the first case of extraconal orbital pleomorphic adenoma arising from ectopic lacrimal gland associated with signs of optic neuropathy.

Keywords: Ectopic lacrimal gland, Optic disc swelling, Orbital tumor, Pleomorphic adenoma

SUPPORTING INFORMATION


Acknowledgments

We thank Htar Htar, Consultant Radiologist, Department of Radiology, Yangon General Hospital, Yangon, Myanmar.

Author Contributions

Zin May Htoon - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published

Ko Ko Thant - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published

Le’ Shwe Zin - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published

Thet Naing - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published

Guaranter of Submission

The corresponding author is the guarantor of submission.

Source of Support

None

Consent Statement

Written informed consent was obtained from the patient for publication of this article.

Data Availability

All relevant data are within the paper and its Supporting Information files.

Conflict of Interest

Authors declare no conflict of interest.

Copyright

© 2019 Zin May Htoon et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.